ORPHA:91385
Acquired angioedema
Also called AAE, Acquired C1 inhibitor deficiency, Acquired angioneurotic edema, Acquired bradykinine-induced angioedema, Acquired non histamine-induced angioedema
- Body system
- Immunological diseases
- Inheritance pattern
- Not applicable
- Typical age of onset
- Adult
- Estimated prevalence
- 1-9 / 1 000 000 (Denmark)
- Rarity class
- 1-9 / 1 000 000
About this disease
A rare disease characterized by the occurrence of transitory and recurrent subcutaneous and/or submucosal edemas resulting in swelling and/or abdominal pain due to an acquired C1 inhibitor (C1-INH) deficiency.
Definition from Orphanet.
Learn more
Source: Orphanet (Orphadata), ORPHA:91385. Data release 2026-06-23. www.orphadata.com — CC BY 4.0.