ORPHA:158057
Acquired hemophagocytic lymphohistiocytosis associated with malignant disease
- Body system
- Immunological diseases
- Inheritance pattern
- Not documented in Orphadata
- Typical age of onset
- All ages
- Estimated prevalence
- Unknown (Worldwide)
- Rarity class
- Unknown
ORPHA:158057 is classified under "Immunological diseases" in the Orphanet nomenclature.
Common signs
- Abnormal circulating interleukin concentration
- Splenomegaly
- Pancytopenia
- Fever
- Immune dysregulation
- Increased circulating ferritin concentration