Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:98916

Acute inflammatory demyelinating polyradiculoneuropathy

Also called AIDP, Acute idiopathic demyelinating polyneuropathy, Acute inflammatory polyneuropathy, GBS, acute inflammatory demyelinating polyradiculoneuropathic form, Guillain-Barré syndrome, acute inflammatory demyelinating polyradiculoneuropathic form

Body system
Neurological diseases
Inheritance pattern
Multigenic/multifactorial, Not applicable
Typical age of onset
All ages
Estimated prevalence
1-9 / 100 000 (Europe)
Rarity class
1-9 / 100 000

ORPHA:98916 is classified under "Neurological diseases" in the Orphanet nomenclature.

Common signs

  • Hyporeflexia
  • Generalized hypotonia
  • Recurrent fever
  • Drooling
  • Unsteady gait
  • EMG: neuropathic changes