Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:693647

Agammaglobulinemia-early-onset hypertrophic cardiomyopathy-neutropenia syndrome

Also called Syndromic agammaglobulinemia due to FNIP1 deficiency, Syndromic hypogammaglobulinemia due to FNIP1 deficiency

Body system
Immunological diseases
Inheritance pattern
Autosomal recessive
Typical age of onset
Infancy, Neonatal
Estimated prevalence
<1 / 1 000 000 (Worldwide)
Rarity class
<1 / 1 000 000

ORPHA:693647 is classified under "Immunological diseases" in the Orphanet nomenclature.

Common signs