Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:363717

Alexander disease type I

Also called AxD type I

Body system
Neurological diseases
Inheritance pattern
Not applicable
Typical age of onset
Infancy, Neonatal
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:363717 is classified under "Neurological diseases" in the Orphanet nomenclature.

Common signs

  • Abnormal cerebral white matter morphology
  • Focal T2 hyperintense basal ganglia lesion
  • Seizure
  • Cerebellar atrophy
  • Failure to thrive
  • Scoliosis