Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:1008

Alopecia-epilepsy-pyorrhea-intellectual disability syndrome

Also called Shokeir syndrome

Body system
Skin diseases
Inheritance pattern
Autosomal dominant
Typical age of onset
Not documented in Orphadata
Estimated prevalence
Not documented in Orphadata
Rarity class
Not documented in Orphadata

ORPHA:1008 is classified under "Skin diseases" in the Orphanet nomenclature.

Common signs

  • Abnormality of the dentition
  • Gingivitis
  • Abnormal eyelash morphology
  • Periodontitis
  • Intellectual disability, mild
  • Sparse scalp hair