Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:1014

Alopecia-intellectual disability-hypergonadotropic hypogonadism syndrome

Also called Devriendt-Vandenberghe-Fryns syndrome

Body system
Skin diseases
Inheritance pattern
Unknown
Typical age of onset
Neonatal
Estimated prevalence
<1 / 1 000 000 (Worldwide)
Rarity class
<1 / 1 000 000

ORPHA:1014 is classified under "Skin diseases" in the Orphanet nomenclature.

Common signs

  • Hypergonadotropic hypogonadism
  • Intellectual disability, mild
  • Alopecia totalis