Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:93

Aspartylglucosaminuria

Also called Aspartylglucosaminidase deficiency

Body system
Neurological diseases
Inheritance pattern
Autosomal recessive
Typical age of onset
Childhood
Estimated prevalence
1-9 / 1 000 000 (Australia)
Rarity class
1-9 / 1 000 000

ORPHA:93 is classified under "Neurological diseases" in the Orphanet nomenclature.

Common signs

  • Gingival overgrowth
  • Mandibular prognathia
  • Hypertelorism
  • Wide nasal bridge
  • Delayed speech and language development
  • Intellectual disability