Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:363429

Autosomal recessive cerebellar ataxia-pyramidal signs-nystagmus-oculomotor apraxia syndrome

Body system
Inborn errors of metabolism
Inheritance pattern
Autosomal recessive
Typical age of onset
Infancy, Neonatal
Estimated prevalence
<1 / 1 000 000 (Worldwide)
Rarity class
<1 / 1 000 000

ORPHA:363429 is classified under "Inborn errors of metabolism" in the Orphanet nomenclature.

Common signs

  • Nystagmus
  • Oculomotor apraxia
  • Progressive cerebellar ataxia
  • Abnormal pyramidal sign
  • Ptosis
  • Optic disc pallor