Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:90280

Chilblain lupus

Body system
Skin diseases
Inheritance pattern
Not applicable
Typical age of onset
Adolescent, Adult, Childhood, Elderly, Infancy
Estimated prevalence
<1 / 1 000 000 (Worldwide)
Rarity class
<1 / 1 000 000

ORPHA:90280 is classified under "Skin diseases" in the Orphanet nomenclature.

Common signs

  • Hyperkeratosis
  • Cutis marmorata
  • Skin rash
  • Rheumatoid factor positive
  • Increased circulating immunoglobulin concentration
  • Inflammatory abnormality of the skin