ORPHA:221
Dermatomyositis
Also called Adult dermatomyositis
- Body system
- Skin diseases
- Inheritance pattern
- Not applicable
- Typical age of onset
- Adult, Elderly
- Estimated prevalence
- 1-9 / 1 000 000 (Australia)
- Rarity class
- 1-9 / 1 000 000
ORPHA:221 is classified under "Skin diseases" in the Orphanet nomenclature.
Common signs
- Edema
- Autoimmunity
- Limb-girdle muscle weakness
- Myalgia
- Proximal muscle weakness
- Inflammatory myopathy