ORPHA:79456
Diffuse cutaneous mastocytosis
Also called DCM, Diffuse cutaneous maculopapulous mastocytosis
- Body system
- Skin diseases
- Inheritance pattern
- Not applicable
- Typical age of onset
- Infancy, Neonatal
- Estimated prevalence
- <1 / 1 000 000 (Worldwide)
- Rarity class
- <1 / 1 000 000
ORPHA:79456 is classified under "Skin diseases" in the Orphanet nomenclature.
Common signs
- Pruritus
- Generalized abnormality of skin
- Darier's sign
- Flushing
- Increased serum mast cell beta-tryptase concentration
- Urticaria