ORPHA:220393
Diffuse cutaneous systemic sclerosis
Also called Diffuse cutaneous systemic scleroderma, Progressive cutaneous systemic scleroderma, Progressive cutaneous systemic sclerosis
- Body system
- Skin diseases
- Inheritance pattern
- Multigenic/multifactorial, Not applicable
- Typical age of onset
- Adult
- Estimated prevalence
- 1-9 / 100 000 (Taiwan, Province of China)
- Rarity class
- 1-9 / 100 000
ORPHA:220393 is classified under "Skin diseases" in the Orphanet nomenclature.
Common signs
- Gastroesophageal reflux
- Dyspnea
- Pulmonary infiltrates
- Autoimmunity
- Oliguria
- Narrow foramen obturatorium