Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:891

Familial exudative vitreoretinopathy

Also called Criswick-Schepens syndrome, FEVR

Body system
Neurological diseases
Inheritance pattern
Autosomal dominant, Autosomal recessive, X-linked recessive
Typical age of onset
Infancy, Neonatal
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:891 is classified under "Neurological diseases" in the Orphanet nomenclature.

Common signs

  • Peripheral retinal avascularization
  • Falciform retinal fold
  • Reduced visual acuity
  • Tractional retinal detachment
  • Abnormality of the optic disc
  • Retinal neovascularization