ORPHA:540

Familial hemophagocytic lymphohistiocytosis

Also called Familial HLH

Body system

Immunological diseases

Inheritance pattern

Autosomal recessive

Typical age of onset

Adolescent, Infancy

Estimated prevalence

1-9 / 100 000 (Sweden)

Rarity class

1-9 / 100 000

ORPHA:540 is classified under "Immunological diseases" in the Orphanet nomenclature.