Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:158048

Hemophagocytic syndrome associated with an infection

Also called IAHS, VAHS, Virus-associated hemophagocytic syndrome

Body system
Immunological diseases
Inheritance pattern
Not documented in Orphadata
Typical age of onset
All ages
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:158048 is classified under "Immunological diseases" in the Orphanet nomenclature.

Common signs

  • Splenomegaly
  • Pancytopenia
  • Fever
  • Abnormal inflammatory response
  • Abnormal T cell subset distribution
  • Abnormal cytokine signaling