Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:95159

Hepatoerythropoietic porphyria

Also called HEP

Body system
Inborn errors of metabolism
Inheritance pattern
Autosomal recessive
Typical age of onset
Childhood
Estimated prevalence
<1 / 1 000 000 (Worldwide)
Rarity class
<1 / 1 000 000

ORPHA:95159 is classified under "Inborn errors of metabolism" in the Orphanet nomenclature.

Common signs

  • Abnormal enzyme/coenzyme activity
  • Severe photosensitivity
  • Abnormal blistering of the skin
  • Fragile skin
  • Red urine
  • Abnormal circulating porphyrin concentration