Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:408

Isolated glycerol kinase deficiency

Also called Hyperglycerolemia

Body system
Inborn errors of metabolism
Inheritance pattern
X-linked recessive
Typical age of onset
All ages
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:408 is classified under "Inborn errors of metabolism" in the Orphanet nomenclature.

Common signs

  • Intellectual disability
  • Hypotonia
  • Global developmental delay
  • Reduced tendon reflexes
  • Metabolic acidosis
  • Abnormality of speech or vocalization