ORPHA:90283
Lupus erythematosus tumidus
Also called Intermittent cutaneous lupus
- Body system
- Skin diseases
- Inheritance pattern
- Not documented in Orphadata
- Typical age of onset
- Adolescent, Adult, Childhood, Elderly
- Estimated prevalence
- Unknown (Worldwide)
- Rarity class
- Unknown
ORPHA:90283 is classified under "Skin diseases" in the Orphanet nomenclature.
Common signs
- Cutaneous photosensitivity
- Erythematous plaque
- Deep dermal perivascular inflammatory infiltrate
- Antinuclear antibody positivity
- Annular cutaneous lesion
- Autoimmune antibody positivity