Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:2398

Multiple symmetric lipomatosis

Also called Cephalothoracic lipodystrophy, Familial benign cervical lipomatosis, Launois-Bensaude lipomatosis, Madelung disease

Body system
Skin diseases
Inheritance pattern
Autosomal dominant, Autosomal recessive, Mitochondrial inheritance, Not applicable
Typical age of onset
Adolescent, Adult, Childhood, Elderly
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:2398 is classified under "Skin diseases" in the Orphanet nomenclature.

Common signs

  • Multiple lipomas
  • Joint stiffness
  • Arthralgia
  • Abnormal adipose tissue morphology
  • Insulin resistance
  • Gait disturbance