Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:624166

Non-specific autoimmune supratentorial encephalitis with characteristic antibodies

Also called Non-specific supratentorial AE with characteristic antibodies

Body system
Neurological diseases
Inheritance pattern
Not applicable
Typical age of onset
All ages
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:624166 is classified under "Neurological diseases" in the Orphanet nomenclature.

Common signs

  • Anti-dachshund family transcription factor 1 antibody positivity
  • Anti-potassium channel tetramerization domain containing 16 antibody positivity
  • Anti-DREBRIN antibody positivity