ORPHA:1183
Opsoclonus-myoclonus syndrome
Also called Ataxo-opso-myoclonus syndrome, Dancing eye syndrome, Dancing eye-dancing feet syndrome, Kinsbourne syndrome, OMA syndrome, OMS, Opsoclonus-myoclonus-ataxia syndrome, POMA syndrome, Paraneoplastic opsoclonus-myoclonus, Paraneoplastic opsoclonus-myoclonus-ataxia syndrome
- Body system
- Neurological diseases
- Inheritance pattern
- Not applicable
- Typical age of onset
- Childhood, Infancy
- Estimated prevalence
- <1 / 1 000 000 (Europe)
- Rarity class
- <1 / 1 000 000
ORPHA:1183 is classified under "Neurological diseases" in the Orphanet nomenclature.
Common signs
- Abnormal saccadic eye movements
- Ataxia
- Myoclonus
- Sleep abnormality
- Opsoclonus
- Anti-Amphiphysin antibody