Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:1183

Opsoclonus-myoclonus syndrome

Also called Ataxo-opso-myoclonus syndrome, Dancing eye syndrome, Dancing eye-dancing feet syndrome, Kinsbourne syndrome, OMA syndrome, OMS, Opsoclonus-myoclonus-ataxia syndrome, POMA syndrome, Paraneoplastic opsoclonus-myoclonus, Paraneoplastic opsoclonus-myoclonus-ataxia syndrome

Body system
Neurological diseases
Inheritance pattern
Not applicable
Typical age of onset
Childhood, Infancy
Estimated prevalence
<1 / 1 000 000 (Europe)
Rarity class
<1 / 1 000 000

ORPHA:1183 is classified under "Neurological diseases" in the Orphanet nomenclature.

Common signs

  • Abnormal saccadic eye movements
  • Ataxia
  • Myoclonus
  • Sleep abnormality
  • Opsoclonus
  • Anti-Amphiphysin antibody