Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:817

Peeling skin syndrome

Also called Deciduous skin, Familial continuous skin peeling syndrome, Idiopathic deciduous skin, Keratosis exfoliativa congenita, PSS, Peeling skin disease

Body system
Skin diseases
Inheritance pattern
Autosomal recessive
Typical age of onset
Infancy, Neonatal
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:817 is classified under "Skin diseases" in the Orphanet nomenclature.

Common signs