Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:240085

Progressive supranuclear palsy-predominant parkinsonism syndrome

Also called PSP-p, PSP-parkinsonism

Body system
Neurological diseases
Inheritance pattern
Not applicable
Typical age of onset
Adult
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:240085 is classified under "Neurological diseases" in the Orphanet nomenclature.

Common signs

  • Postural instability
  • Parkinsonism with favorable response to dopaminergic medication
  • Vertical supranuclear gaze palsy
  • Abnormal saccadic eye movements
  • Bradykinesia
  • Axial muscle stiffness