Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:100057

Renin-angiotensin-aldosterone system-blocker-induced angioedema

Also called ACE inhibitor-related acquired angioedema, ACEI-related acquired angioedema, Acquired angioedema with normal C1 inhibitor, Acquired angioedema with normal C1INH, RAAS-blocker-induced angioedema, RAAS-blocker-induced angioneurotic edema, RAE, Renin-angiotensin-aldosterone system-blocker-induced angioneurotic edema

Body system
Immunological diseases
Inheritance pattern
Multigenic/multifactorial, Not applicable
Typical age of onset
Adult
Estimated prevalence
Unknown (Worldwide)
Rarity class
Unknown

ORPHA:100057 is classified under "Immunological diseases" in the Orphanet nomenclature.

Common signs

  • Facial edema
  • Abnormal capillary physiology
  • Respiratory distress
  • Swollen lip
  • Tongue edema
  • Palpebral edema