Rare Zebra

Rare disease search prototype built on Orphanet data

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ORPHA:93474

Scheie syndrome

Also called MPS1S, MPSIS, Mucopolysaccharidosis type 1S, Mucopolysaccharidosis type IS

Body system
Bone diseases
Inheritance pattern
Autosomal recessive
Typical age of onset
Adolescent, Adult, Childhood
Estimated prevalence
1-9 / 1 000 000 (Canada)
Rarity class
1-9 / 1 000 000

ORPHA:93474 is classified under "Bone diseases" in the Orphanet nomenclature.

Common signs

  • Glaucoma
  • Abnormality of the skeletal system
  • Limitation of joint mobility
  • Aortic regurgitation
  • Corneal opacity
  • Mucopolysacchariduria