Rare Zebra

Rare disease search prototype built on Orphanet data

← Back to search

ORPHA:93357

SPONASTRIME dysplasia

Also called Spondylar and nasal changes with striations of the metaphyses (SPONASTRIME) dysplasia, Spondyloepimetaphyseal dysplasia, Sponastrime type

Body system
Bone diseases
Inheritance pattern
Autosomal recessive
Typical age of onset
Infancy, Neonatal
Estimated prevalence
<1 / 1 000 000 (Worldwide)
Rarity class
<1 / 1 000 000

ORPHA:93357 is classified under "Bone diseases" in the Orphanet nomenclature.

Common signs

  • Abnormality of the vertebral column
  • Platyspondyly
  • Abnormal facial shape
  • Depressed nasal bridge
  • Disproportionate short-limb short stature
  • Midface retrusion